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    磷酸半乳糖尿苷酸轉移酶1抗體
    • 產品貨號:
      BN40986R
    • 中文名稱:
      磷酸半乳糖尿苷酸轉移酶1抗體
    • 英文名稱:
      Rabbit anti-GALT Polyclonal antibody
    • 品牌:
      Biorigin
    • 貨號

      產品規格

      售價

      備注

    • BN40986R-100ul

      100ul

      ¥2360.00

      交叉反應:Mouse,Rat(predicted:Human,Cow) 推薦應用:WB,IHC-P,IHC-F,ELISA

    • BN40986R-200ul

      200ul

      ¥3490.00

      交叉反應:Mouse,Rat(predicted:Human,Cow) 推薦應用:WB,IHC-P,IHC-F,ELISA

    產品描述

    英文名稱GALT
    中文名稱磷酸半乳糖尿苷酸轉移酶1抗體
    別    名Gal 1 P uridylyltransferase; Galactose 1 phosphate uridyl transferase; Galactose 1 phosphate uridylyltransferase; UDP glucose hexose 1 phosphate uridylyltransferase; GALT_HUMAN.  
    研究領域腫瘤  細胞生物  免疫學  激酶和磷酸酶  
    抗體來源Rabbit
    克隆類型Polyclonal
    交叉反應Mouse, Rat,  (predicted: Human, Cow, )
    產品應用WB=1:500-2000 ELISA=1:5000-10000 IHC-P=1:100-500 IHC-F=1:100-500 (石蠟切片需做抗原修復)
    not yet tested in other applications.
    optimal dilutions/concentrations should be determined by the end user.
    分 子 量43kDa
    細胞定位細胞漿 
    性    狀Liquid
    濃    度1mg/ml
    免 疫 原KLH conjugated synthetic peptide derived from human GALT:251-350/379 
    亞    型IgG
    純化方法affinity purified by Protein A
    儲 存 液0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
    保存條件Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
    PubMedPubMed
    產品介紹GALT (Galactose 1 phosphate uridyl transferase) catalyzes the second step of the Leloir pathway of galactose metabolism, namely the conversion of UDP glucose + galactose 1 phosphate to glucose 1 phosphate + UDP galactose. The absence of this enzyme results in classic galactosemia in humans and can be fatal in the newborn period if lactose is not removed from the diet. The pathophysiology of galactosemia has not been clearly defined.

    Subunit:
    Homodimer (Probable).

    DISEASE:
    Defects in GALT are the cause of galactosemia (GALCT) [MIM:230400]. Galactosemia is an inherited disorder of galactose metabolism that causes jaundice, cataracts, and mental retardation.

    Similarity:
    Belongs to the galactose-1-phosphate uridylyltransferase type 1 family.

    SWISS:
    P07902

    Gene ID:
    2592

    Database links:

    Entrez Gene: 2592 Human

    Entrez Gene: 14430 Mouse

    Entrez Gene: 298003 Rat

    Omim: 606999 Human

    SwissProt: P07902 Human

    SwissProt: Q03249 Mouse

    SwissProt: P43424 Rat

    Unigene: 522090 Human

    Unigene: 439669 Mouse

    Unigene: 102781 Rat



    Important Note:
    This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.


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