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    鉀離子通道蛋白家族成員1樣蛋白抗體
    • 產品貨號:
      BN41415R
    • 中文名稱:
      鉀離子通道蛋白家族成員1樣蛋白抗體
    • 英文名稱:
      Rabbit anti-KCNE1L Polyclonal antibody
    • 品牌:
      Biorigin
    • 貨號

      產品規格

      售價

      備注

    • BN41415R-100ul

      100ul

      ¥2360.00

      交叉反應:Human(predicted:Mouse,Rat,Pig,Cow,Rabbit,Sheep) 推薦應用:WB,IHC-P,IHC-F,IF,Flow-Cyt,ELISA

    • BN41415R-200ul

      200ul

      ¥3490.00

      交叉反應:Human(predicted:Mouse,Rat,Pig,Cow,Rabbit,Sheep) 推薦應用:WB,IHC-P,IHC-F,IF,Flow-Cyt,ELISA

    產品描述

    英文名稱KCNE1L
    中文名稱鉀離子通道蛋白家族成員1樣蛋白抗體
    別    名AMME syndrome candidate gene 2 protein; AMMECR2 protein; Cardiac voltage gated potassium channel accessory subunit 5; KCNE1 like; KCNE5; Mink; MinK like protein; Potassium voltage gated channel subfamily E member 1 like protein; Potassium voltage gated channel, Isk related family, member 1 like; Voltage gated potassium channel accessory subunit 5; KCE1L_HUMAN.  
    研究領域心血管  神經生物學  通道蛋白  
    抗體來源Rabbit
    克隆類型Polyclonal
    交叉反應Human,  (predicted: Mouse, Rat, Pig, Cow, Rabbit, Sheep, )
    產品應用WB=1:500-2000 ELISA=1:5000-10000 IHC-P=1:100-500 IHC-F=1:100-500 Flow-Cyt=1ug/test IF=1:50-200 (石蠟切片需做抗原修復)
    not yet tested in other applications.
    optimal dilutions/concentrations should be determined by the end user.
    分 子 量15kDa
    細胞定位細胞漿 細胞膜 
    性    狀Liquid
    濃    度1mg/ml
    免 疫 原KLH conjugated synthetic peptide derived from human KCNE1L:11-110/142 <Extracellular>
    亞    型IgG
    純化方法affinity purified by Protein A
    儲 存 液0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
    保存條件Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
    PubMedPubMed
    產品介紹KCNE1L belongs to the potassium channel KCNE family which represent the most complex class of voltage-gated ion channels from both functional and structural standpoints. Their diverse functions include regulating neurotransmitter release, heart rate, insulin secretion, neuronal excitability, epithelial electrolyte transport, smooth muscle contraction, and cell volume.

    Subcellular Location:
    Plasma membrane; Single-pass type I membrane protein.

    Tissue Specificity:
    Highly expressed in heart, skeletal muscle, brain, spinal cord and placenta.

    DISEASE:
    Defects in KCNE1L are involved in Alport syndrome with mental retardation midface hypoplasia and elliptocytosis (ATS-MR) [MIM:300194]. A X-linked contiguous gene deletion syndrome characterized by glomerulonephritis, deafness, mental retardation, midface hypoplasia and elliptocytosis.

    Similarity:
    Belongs to the potassium channel KCNE family.

    SWISS:
    Q9UJ90

    Gene ID:
    23630

    Database links:

    Entrez Gene: 23630 Human

    Omim: 300328 Human

    SwissProt: Q9UJ90 Human



    Important Note:
    This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.











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